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Relationship Between Mitochondrial Structure and Bioenergetics in Pseudoxanthoma elasticum Dermal Fibroblasts.
Lofaro, Francesco-Demetrio; Boraldi, Federica; García-Fernández, María Inmaculada; Lara, Estrella; Valdivielso-Felices, Pedro
; Quaglino, Daniela[et al.] (Frontiers Media, 2020-12-17)
PXE is a genetic disease considered as a paradigm of ectopic mineralization disorders, being characterized by multisystem clinical manifestations due to progressive calcification of skin, eyes, and the cardiovascular system, ...